Dermatofibrosarcoma protuberans in childhood.

Dermatofibrosarcoma Protuberans in Childhood

[Myxoid dermatofibrosarcoma protuberans in childhood].

Dermatofibrosarcoma protuberans is a locally aggressive skin tumor that affects young and middle-aged adults. A number of histological variants have been described, the myxoid type being one of the least common. Microscopically it is formed of a neoplastic growth that is located in the dermis and hypodermis and has a predominant myxoid component. Peripherally there are infiltrating bundles of s...

Case report: Pedunculated Dermatofibrosarcoma Protuberans from Kerman

Dermatofibrosarcoma protuberans is a tumor of intermediate malignancy characterized by its aggressive local growth and marked propensity to recur after surgical excision. Many forms of the tumor has been reported. We report a pedunculated form of tumor. A 45-year-old woman felt a growing tumor on her trunk for 6 years but did not seek medical consultation until it had ulcerated 6 months ago. Sk...

Myxoid Dermatofibrosarcoma Protuberans of the Vulva with Myoid Nodules: Clinicopathologic and Immunohistochemical Study of a Case

Dermatofibrosarcoma protuberans is a slow growing dermal spindle cell tumor seldom seen in the vulva and its myxoid variant, a rare type of dermatofibrosarcoma protuberans is characterised by extensive myxoid degeneration. We present the case of a 62 year old woman with an enlarging vulval swelling. Mass was excised surgically. Histopathologically the tumor consisted of uniform spindle-shaped c...

Magnetic resonance imaging and mammographic appearance of dermatofibrosarcoma protuberans in a male breast: a case report and literature review

INTRODUCTION Dermatofibrosarcoma protuberans is a rare low-grade soft tissue neoplasm with trunk and extremities being the most common sites of involvement. We report a rare case of male breast with dermatofibrosarcoma protuberans and its imaging features. To our knowledge the imaging appearance of dermatofibrosarcoma protuberans of the breast has never been reported in the literature. CASE P...